Dentinogenesis imperfecta: case report and review of literature

• Author Details:   
• Rupam Sinha
• Soumyabrata Sarkar
• Tanya Khaitan
• Arpita Kabiraj
• Soumi Ghanta
• Deepsikha Ramani

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Dentinogenesis imperfecta (DI) is one of the most common hereditary disorders of dentin formation. It follows an autosomal dominant pattern of transmission, affecting both the formation and mineralization of dentin. Either or both primary and permanent dentition is affected by it. It is characterized by the presence of opalescent dentin, resulting in a dusky blue to brownish discoloration of the teeth. Here we present a case of DI in a 20 year old female with remarkable clinical, radiological and histological presentation.

Keywords: Autosomal; Dentin; Odontoblasts; Opalescent